Rosai-Dorfman Disease or sinus histiocytosis with massive lymphadenopathy
Keywords:
Rosai-Dorman disease, sinus histiocytosis, therapeutics.Abstract
Rosai-Dorfman Disease,or sinus histiocytosis with massive lymphadenopathy,is a chronic histiocytic spreading disorder with a benign process which in the majority of the cases has a tendency to spontaneous regression. The etiology is still unknown. It may affect both genders but it is predominant on men at their first and second decades of life. Even though it is characterized by a lymph node condition, it also compromises other organs such as skin, respiratory tract, urinary system, bones and the central nervous system. Skin injuries are generally numerous and unspecified. A male patient is introduced with Rosai-Dorman disease presenting bilateral cervical lymph nodes, elbow and ankle arthralgia and erythematic tumors on face. He was treated with intra-lesion corticosteroids and systemics with favorable evolution.
Author Biographies
Lina Primo
Médica, becaria de tercer año, División de Dermatología, Hospital de Clínicas “José de San Martín”, Facultad de Medicina, Universidad de Buenos Aires, Buenos Aires, Argentina
Maximiliano Mestroni
Médico dermatólogo, exjefe de residentes, División de Dermatología, Hospital de Clínicas “José de San Martín”, Facultad de Medicina, Universidad de Buenos Aires, Buenos Aires, Argentina
Miguel Allevato
Médico dermatólogo; jefe, División de Dermatología, Hospital de Clínicas “José de San Martín”, Facultad de Medicina, Universidad de Buenos Aires, Buenos Aires, Argentina
Mario Marini
Médico dermatólogo; profesor titular consultor de Dermatología, División de Dermatología, Hospital de Clínicas “José de San Martín”, Facultad de Medicina, Universidad de Buenos Aires, Buenos Aires, Argentina
Alberto Devés
Médico patólogo, Departamento de Patología, Hospital de Clínicas “José de San Martín”, Facultad de Medicina, Universidad de Buenos Aires, Buenos
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