Melkersson-Rosenthal’s syndrome

Authors

  • Alberto Enrique Saponaro
  • Tomás Mosquera
  • Mario Alberto Marini3
  • Félix Vigovich

Keywords:

Melkersson-Rosenthal, Melkersson-Rosenthal syndrome, granulomatous cheilitis, facial paralysis.

Abstract

Melkersson-Rosenthal syndrome is an affection of unknown origin, characterized by a classic triad: recurrent oro-facial swelling, recurrent peripheral facial paralysis and fissured tongue. We present a case in a 35 year old man.

Author Biographies

Alberto Enrique Saponaro

Médico dermatólogo; jefe del Servicio de Dermatología; profesor titular de Dermatología, Universidad Católica Argentina, Hospital Británico de Buenos Aires, Argentina.

Tomás Mosquera

Médico de planta, Servicio de Dermatología, Hospital Británico de Buenos Aires, Argentina.

Mario Alberto Marini3

Médico consultor, Servicio de Dermatología; profesor titular de Dermatología, Universidad de Buenos Aires, Hospital Británico de Buenos Aires, Argentina.

Félix Vigovich

Médico de planta, Servicio de Patología, Hospital Británico de Buenos Aires, Argentina.

References

1. Scully C, Hegarty A. The oral cavity and lips. En: Burns T, Breathnach S, Cox N, Griffiths C. Rook’s textbook of dermatology. West Sussex: Ed. Wiley-Blackwell, 2010. p. 125-6.
2. Rogers RS 3r. Melkersson-Rosenthal syndrome and orofacial granulomatosis. Dermatol Clin. 1996;14:371-9.
3. Banks T, Gada S. A comprehensive review of current treatments for granulomatous cheilitis. Br J Dermatol. 2012;166:934-7.
4. Zeng W, Geng S, Niu X, Yuan J. Complete Melkersson-Rosenthal syndrome with multiple cranial nerve palsies. Clin Exp Dermatol. 2010;35:272-4.
5. Pietropaolo N, Villalba I, Ramos L, Mercado Y, Kowalczuc A, Galimberti R. Queilitis granulomatosa: a propósito de un caso. Dermatol Argent. 2003;9:112-5.
6. Lynde CB, Bruce AJ, Orvidas LJ, Rogers RS 3rd, Depry JL. Cheilitis granulomatosa treated with intralesional corticosteroids and anti-inflammatory agents. J Am Acad Dermatol. 2011 Sep;65(3):e101-2.
7. Oudrhiri L, Chiheb S, Marnissi F, Zamiati S, Benchikhi H. Successful treatment of Miescher’s cheilitis in Melkersson-Rosenthal syndrome with betamethasone injections and doxycycline. Pan Afr Med J. 2012;13:75.

How to Cite

1.
Saponaro AE, Mosquera T, Marini3 MA, Vigovich F. Melkersson-Rosenthal’s syndrome. rev. asoc. colomb. dermatol. cir. dematol. [Internet]. 2019 Aug. 9 [cited 2024 Jul. 22];22(2):159-61. Available from: https://revista.asocolderma.org.co/index.php/asocolderma/article/view/1046

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Published

2019-08-09

How to Cite

1.
Saponaro AE, Mosquera T, Marini3 MA, Vigovich F. Melkersson-Rosenthal’s syndrome. rev. asoc. colomb. dermatol. cir. dematol. [Internet]. 2019 Aug. 9 [cited 2024 Jul. 22];22(2):159-61. Available from: https://revista.asocolderma.org.co/index.php/asocolderma/article/view/1046

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Section

Case Report
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