Colagenomas: manifestación cutánea de neoplasia endocrina múltiple tipo 1 (MEN 1)
DOI:
https://doi.org/10.29176/2590843X.1539Keywords:
Skin and connective tissue diseases, Skin neoplasms, Multiple endocrine neoplasia type 1Abstract
Multiple endocrine neoplasia type 1 is a rare hereditary syndrome characterized by parathyroid, anterior pituitary and pancreatic tumors, that may also be associated with benign cutaneous neoplasms like angiofibromas and collagenomas, that can precede endocrine manifestations.
We present the case of a 23-year-old female patient with primary hyperparathyroidism, Cushing disease and a pancreatic neuroendocrine tumor associated with multiple collagenomas that appeared before systemic symptoms.
Author Biographies
Laura Pulgarín
Médico general, Universidad de Antioquia. Residente de Dermatología, Universidad del Valle.
Simón Gallo
Médico general. Residente de Dermatología, Centro de Investigaciones Dermatológicas CIDERM, Sección de Dermatología, Facultad de Medicina, Universidad de Antioquia.
Natalia Giraldo
Médico general. Residente de Dermatología, Centro de Investigaciones Dermatológicas CIDERM, Sección de Dermatología, Facultad de Medicina, Universidad de Antioquia.
Carlos Montealegre
Médico dermatólogo, Centro de Investigaciones Dermatológicas CIDERM, Sección de Dermatología, Facultad de Medicina, Universidad de Antioquia.
Alejandro Roman-González
Médico endocrinólogo, Universidad de Antioquia, Hospital Universitario San Vicente Fundación.
References
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