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Diagnosis: systemic lupus erythematosus with toxic epidermal necrolysis-like manifestation
DOI:
https://doi.org/10.29176/2590843X.1767Keywords:
Lupus eritematoso cutáneo; Lupus eritematoso sistémico; Necrólisis epidérmica tóxica; Síndrome de Stevens JohnsonAbstract
A middle-aged woman presented with immunological, mucocutaneous, hematological and renal signs and symptoms, with a final diagnosis of systemic lupus erythematosus with toxic epidermal necrolysis (TEN) type manifestation. Systemic lupus erythematosus is accompanied by multiple dermatological manifestations, of these, different forms of bullous lesions have been described, including lupus erythematosus with TEN-type manifestation, an entity with lower morbidity and mortality than classic TEN and which normally presents an excellent response to systemic corticosteroids. The presentation of this clinical case is considered relevant due to its rarity and because it can be an important clue for the diagnosis of systemic lupus
erythematosus.
References
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