Senear Usher syndrome, a rare variant of pemphigus foliaceus
DOI:
https://doi.org/10.29176/2590843X.1818Keywords:
Pemphigus, blisters, hyperpigmentationAbstract
Senear-Usher syndrome is a localized variant of pemphigus foliaceus, rare, with a chronic course, manifested by well-defined erythematous squamous plaques, with a seborrheic appearance and distribution, which adopts a butterfly-wing pattern resembling cutaneous lupus erythematosus (characteristic in our case) positive Nikolsky sign. With the presence of fragile and fleeting blisters, it does not affect the mucosa, it is a disease of low incidence and represents 0.5 to 3.2 cases per 100,000 inhabitants per year. In ages 15-84 years, on average at 54 years, without predominance of race or sex. We present the case of a 31-year-old male patient, skin phototype V/VI according to Fitzpatrick, with no significant history, presenting bilateral and symmetrical generalized dermatosis beginning in the central facial region characterized by well-defined erythematous plaques with regular borders, with Presence of thick oily yellow scales and bruises on the surface, which spread to other seborrheic areas of the chest, anterior and posterior, exulcerated areas, hyperpigmented macules of variable sizes, pruritic with a 1-year history. A skin biopsy was performed with findings consistent with this disease. Treatment with topical and systemic steroids and immunosuppressants was started with a good response. A case is reported because it is a rare variant of pemphigus foliaceus, so it is important to report this case in Venezuela.
Author Biographies
Mary Soto, 128245
Médico, residente de segundo año del posgrado de Dermatología. Universidad de Carabobo, Ciudad Hospitalaria “Dr. Enrique Tejera”, Valencia, Estado Carabobo, Valencia, Venezuela.
Neiris Villegas, Universidad de Carabobo
Médico, residente de tercer año del posgrado de Dermatología. Universidad de Carabobo, Ciudad Hospitalaria “Dr. Enrique Tejera”, Valencia, Estado Carabobo, Valencia, Venezuela.
Sandra Vivas, Universidad de Carabobo
Médico internista y dermatóloga. Magíster en Investigación Educativa. Jefa, Servicio de Dermatología, Universidad de Carabobo, Ciudad Hospitalaria “Dr. Enrique Tejera”. Coordinadora, programa de posgrado de Dermatología. Miembro, Sociedad Venezolana de Dermatología; Sociedad Internacional de Dermatoscopia.
References
Vera L, Galavis J, Lander A. Pénfigo eritematoso. Reporte de caso. 2017;11:22–6. Disponible en URL: http://www.umng.edu.co/documents/10162/799732/11Revista+Med+Vol+22+No.1+Enero+Junio+2014.pdf.
Medina D, Navarrete G, Eng A, Cortéz N, Herbas O, Peñaloza Á, et al. Pénfigo seborreico localizado: descripción de seis casos 2008;6:93–8. Disponible en URL: https://www.medigraphic.com/pdfs/cosmetica/dcm-2008/dcm082c.pdf
Cifuentes-tang L, Pineda-pino Y, Victoria-chaparro J. Pénfigo foliáceo subtipo eritematoso. dermatol revista mex. 2019;63:331–6. disponible en URL: https://dermatologiarevistamexicana.org.mx/article/penfigo-foliaceo-subtipo-eritematoso/
Cardillo F, Persand M, Rossi C, Taboada V, Giuliani A. Pénfigo foliáceo tratado con rituximab. Rev Dermatología Argentina Vol. 28 (1): Enero-marzo de 2022: 40-42. https://doi.org/10.47196/da.v28i1.2175
Arenas C, Serrato I. Pénfigo foliáceo variedad seborreica: reporte de un caso pemphigus foliaceus seborrheic variety: a case report. revista med 2014; (1) 22: 73–7. Disponible en URL : http://www.scielo.org.co/pdf/med/v22n1/v22n1a11
Flood D, Lezanski-Gujda A, Miletta NR. Diagnosing Pemphigus Foliaceus: A Rare Blistering Disease Masquerading as a Common Dermatologic Disorder. Mil Med. 2019 May 1;184(5-6):e455-e457. doi: 10.1093/milmed/usy224.
Elizondo C, Tung J, Blanco F. Penfigo Vulgar y Foliaceo: Una revisión bibliográfica. Rev Clínica Esc Med UCR-HSJD 2019;9:48–55. disponible en URL: https://www.medigraphic.com/pdfs/revcliescmed/ucr-2019/ucr191f.pdf
How to Cite
Downloads
Downloads
Published
How to Cite
Issue
Section
License
Copyright (c) 2024 Revista de la Asociación Colombiana de Dermatología y Cirugía Dermatológica
This work is licensed under a Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International License.
Article metrics | |
---|---|
Abstract views | |
Galley vies | |
PDF Views | |
HTML views | |
Other views |