Adult Langerhans cell histiocytosis
Keywords:
Histiocytosis, Langerhans cells, adult Langerhans cell histiocytosisAbstract
Langerhans cell histiocytosis, previously called histiocytosis X, is a disease characterized by the proliferation of CD1a dendritic cells. Its nature, reactive or neoplastic, is still discussed. Its onset in adulthood is uncommon. Its clinical presentation is varied. Langerhans cell histiocytosis is classified as monosystemic (commitment to a single organ, unifocal or multifocal) and multisystemic (involvement of two or more organs, which is subdivided into low and high risk in relation to the organs involved).
We present a patient with low risk multisystemic adult Langerhans cell histiocytosis (bone and skin involvement only).
Author Biographies
Lucrecia Infante
División de Dermatología, Hospital de Clínicas “José de San Martín”, Buenos Aires, Argentina
Juliana Martínez del Sel
Médica de planta, División de Dermatología, Hospital de Clínicas “José de San Martín” Buenos Aires, Argentina
Estefanía Cesaroni
División de Dermatología, Hospital de Clínicas “José de San Martín”, Buenos Aires, Argentina
Lucila Donatti
Médica de planta, División de Dermatología, Hospital de Clínicas “José de San Martín” Buenos Aires, Argentina
Miguel Allevato
Jefe, División de Dermatología, Hospital de Clínicas “José de San Martín”, Buenos Aires, Argentina
Mario Marini
Médico consultor, Universidad de Buenos Aires Buenos Aires, Argentina
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