Fogo selvagem: report of two cases and review of literature

Authors

  • Carolina Cortés
  • Elkin Peñaranda
  • Marcela Rodríguez

Keywords:

Pemphigus, blisters, desmoglein 1

Abstract

Fogo selvagem is an endemic form of pemphigus foliaceus with its own demographic characteristics. It presents in children and teenagers and it is characterized by subcorneal blisters due to auto-antibodies against desmoglein 1. We
report two patients from the Colombian Amazon region with this diagnosis.

Author Biographies

Carolina Cortés

Médicos dermatólogo, Universidad Nacional de Colombia, Bogotá, D.C., Colombia

Elkin Peñaranda

Médicos dermatólogo, Universidad Nacional de Colombia, Bogotá, D.C., Colombia

Marcela Rodríguez

Médica, residente de Dermatología, Pontificia Universidad Javeriana, Bogotá, D.C., Colombia

References

1. Bystryn JC, Rudolph JL. Pemphigus. Lancet. 2005;366:61-73.
2. Galarza C, Ortega A, Ramos W, Hurtado J, Lindo G, Ávila J, et al. Pénfigo foliáceo endémico y pénfigo vulgar en pacientes de edad pediátrica en Uyucali. Dermatología Peruana. 2004;14:99-103.
3. Flores G, Qian Y, Díaz LA. The enigmatic autoimmune response in endemic pemphigus foliaceus. Actas Dermosifiliologr. 2009;100(Supl.2):40-8.
4. Culton DA, QuianY, Li N, Rubestein, Aoki V, Filhio GH, et al. Advances in pemphigus and its endemic pemphigus foliaceus (fogo selvagem) phenotype: A paradigm of human autoimmunity. J Autoimmun. 2008;31:311-24.
5. Abreu AM, Ávila I, Segovia J, Yepes M, Bollag W. Rare clinical form in two patients affected by a new variant of endemic pemphigus in Northern Colombia. SKINmed. 2004;3:317-21.
6. Cunha P, Regina S. Autoinmmune bullous dermatoses. An Bras Dermatol. 2009;84:111-24.
7. Cuhna P, Bystrin JC, Palmeira E, Olieviera J. Sensivity of indirect immunofluoresce and ELISA in detecting intercellular antibodies in endemic pemphigus (fogo selvagem). Int J Dermatol. 2006;45:914-8.
8. Harman KE, Albert S, Black MM. Guidelines for the management of pemphigus vulgaris. Br J Dermatol. 2003;149:926-37.
9. Schmidt E, Goebeler M, Zillikens D. Rituximab in severe pemphigus. Ann NY Acad Sci. 2009;1173:683-91.

How to Cite

1.
Cortés C, Peñaranda E, Rodríguez M. Fogo selvagem: report of two cases and review of literature. rev. asoc. colomb. dermatol. cir. dematol. [Internet]. 2019 Feb. 18 [cited 2024 Jul. 3];20(2):183-6. Available from: https://revista.asocolderma.org.co/index.php/asocolderma/article/view/226

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Published

2019-02-18

How to Cite

1.
Cortés C, Peñaranda E, Rodríguez M. Fogo selvagem: report of two cases and review of literature. rev. asoc. colomb. dermatol. cir. dematol. [Internet]. 2019 Feb. 18 [cited 2024 Jul. 3];20(2):183-6. Available from: https://revista.asocolderma.org.co/index.php/asocolderma/article/view/226

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Case Report
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