Juvenile subacute cutaneous lupus erythematosus with systemic repercussions
DOI:
https://doi.org/10.29176/2590843X.314Keywords:
lupus eritematoso cutáneo subagudo, lupus eritematoso sistémico, patrón anular,, patrón psoriasiformeAbstract
We report the case of a 12-year-old patient with a 3 month clinical history of plaques on skin of the face, nasal dorsum and ears, annular erythematous plaques in trunk, back, upper and lower extremities, erythematous micropapules, some confluent and not pruritic, and in mouth, painless canker sores. Also, had photosensitivity and constitutional symptoms (fever, weight loss)
Laboratory tests evidenced hematological compromise (leukopenia, lymphopenia), the direct Coombs test was positive (without anemia) and there was hypocomplementemia (low C3). The immunoserological profile found positive dappled and cytoplasmic antinuclear antibodies and positive antibodies against extractable nuclear antigens. The skin biopsy reported subacute cutaneous lupus erythematosus.
The patient met criteria for systemic lupus erythematosus and was treated with systemic steroids.
Author Biographies
Luz Vásquez
Médica dermatóloga, Hospital Pablo Tobón Uribe, Medellín, Colombia
Sneider Torres-Soto
Médico, Universidad Pontificia Bolivariana, Medellín, Colombia
Ana Cristina Ruiz
Médica dermatopatóloga, Hospital Pablo Tobón Uribe, Medellín, Colombia.
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