Pigmented dermatofibrosarcoma protuberans (Bednar tumor)

Authors

  • Mariam Rolón
  • José Leonor Tovar
  • Carolina Hernández

Keywords:

dermatofibrosarcoma, pigmented, immunohistochemistry

Abstract

Dermatofibrosarcoma protuberans is a locally aggressive skin tumor. In addition to the conventional type, several morphologic variants have been described and Bednar tumor is one of them. We report herein a peculiar case of pigmented dermatofibrosarcoma protuberans (Bednar tumor), a distinctive pattern. The tumor occurred in a 23-year-old woman who presented with a lesion on her left suprascapular area of 10 years of history.

Author Biographies

Mariam Rolón

Médica dermatopatóloga, Instituto Nacional de Cancerología, Bogotá, D.C., Colombia

José Leonor Tovar

Médico, residente de II año, Departamento de Patología, Fundación Universitaria de Ciencias de la Salud, Bogotá, D.C., Colombia

Carolina Hernández

Médica, residente de III año, Departamento de Dermatología, Pontificia Universidad Javeriana, Bogotá, D.C., Colombia

References

1. Patnayak R, Prayaga A, Anuradha S, Ahmed F, Jena A, Gupta V. Pigmented dermatofibrosarcoma protuberance (Bednar tumor). Eur J Dermatol. 2008;18:98-100.
2. Lee MS, Kang MJ, Kim MY, Kim HO, Song KY, Park YM. Congenital Bednar tumour (pigmented dermatofibrosarcoma protuberans). J Eur Acad Dermatol Venereol. 2008;22:509-11.
3. Kagoura M, Toyoda M, Nagahori H, Makino T, Morohashi M. An ultrastructural and immunohistochemical study of pigmented dermatofibrosarcoma protuberans (Bednar tumor). Eur J Dermatol. 1999;9:366-9.
4. Kini H, Raghuveer CV, Pai MR, SK. Fibrosarcomatous Bednar tumor with distant metastases –a case report. Indian J Pathol Microbiol. 2004;47:26-9.
5. Wang J, Yang W. Pigmented dermatofibrosarcoma protuberans with prominent meningothelial-like whorls. J Cutan Pathol. 2008;35(Suppl.1):65-9.
6. James W, Berger T. Andrews’ Diseases of the Skin. Clinical dermatology. Tenth edition. Canada: Saunders Elsevier; 2006. p. 612.

How to Cite

1.
Rolón M, Tovar JL, Hernández C. Pigmented dermatofibrosarcoma protuberans (Bednar tumor). rev. asoc. colomb. dermatol. cir. dematol. [Internet]. 2019 Feb. 27 [cited 2024 Jul. 3];18(4):233-5. Available from: https://revista.asocolderma.org.co/index.php/asocolderma/article/view/339

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Published

2019-02-27

How to Cite

1.
Rolón M, Tovar JL, Hernández C. Pigmented dermatofibrosarcoma protuberans (Bednar tumor). rev. asoc. colomb. dermatol. cir. dematol. [Internet]. 2019 Feb. 27 [cited 2024 Jul. 3];18(4):233-5. Available from: https://revista.asocolderma.org.co/index.php/asocolderma/article/view/339
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