Pigmented dermatofibrosarcoma protuberans (Bednar tumor)
Keywords:
dermatofibrosarcoma, pigmented, immunohistochemistryAbstract
Dermatofibrosarcoma protuberans is a locally aggressive skin tumor. In addition to the conventional type, several morphologic variants have been described and Bednar tumor is one of them. We report herein a peculiar case of pigmented dermatofibrosarcoma protuberans (Bednar tumor), a distinctive pattern. The tumor occurred in a 23-year-old woman who presented with a lesion on her left suprascapular area of 10 years of history.
Author Biographies
Mariam Rolón
Médica dermatopatóloga, Instituto Nacional de Cancerología, Bogotá, D.C., Colombia
José Leonor Tovar
Médico, residente de II año, Departamento de Patología, Fundación Universitaria de Ciencias de la Salud, Bogotá, D.C., Colombia
Carolina Hernández
Médica, residente de III año, Departamento de Dermatología, Pontificia Universidad Javeriana, Bogotá, D.C., Colombia
References
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3. Kagoura M, Toyoda M, Nagahori H, Makino T, Morohashi M. An ultrastructural and immunohistochemical study of pigmented dermatofibrosarcoma protuberans (Bednar tumor). Eur J Dermatol. 1999;9:366-9.
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5. Wang J, Yang W. Pigmented dermatofibrosarcoma protuberans with prominent meningothelial-like whorls. J Cutan Pathol. 2008;35(Suppl.1):65-9.
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