Primary hypertrophic osteoarthropathy
Keywords:
primary hypertrophic osteoarthropathy, joints, pathological dilatationAbstract
Primary hypertrophic osteoarthropathy, pachydermoperiostosis, is a rare genodermatosis. It is characterized by the triad of pachydermia, digital and periostosis changes. This article reports a patient aged 16 with clinical pachydermoperiostosis who also presents with pyelocaliceal ectasia. This association had not been reported previously.
Author Biographies
María Isabel Moreno
Médica residente II año Dermatología. Pontificia Universidad Javeriana
Carolina Cortés
Dermatóloga. Docente. Hospital Universitario San Rafael
Elkin Omar Peñaranda
Dermatólogo Oncólogo. Docente. Hospital Universitario San Rafael
References
2. Santos DJ, Yuste Ch M, Martínez GO, Alonso SP, Sánchez EJ. Paquidermoperiostosis (síndrome de Touraine-Solente-Golé). Descripción de un caso. Actas Dermosifiliogr. 2007;98:116-20.
3. Latos BA, Marik I, Kuklik M, Materna KA, Povysil C, Kozlowski K. Pachydermoperiostosis –critical analysis with report of five unusual cases. Eur J Pediatr. 2007;166:1237-43.
4. Rastogi R, Suma GN , Prakash R, Chandra RU, Bhargava S, Rastogi V. Pachydermoperiostosis or primary hypertrophic osteoarthropathy: A rare clinic radiologic case. Indian J Radiol Imaging. 2009;19:123-6.
5. Nuñes CT, Rodrigues C, Fraguas FS, Bittencourt CM, Santos TK, Jimenes C. Osteoartropatia hipertrófica primária (paquidermoperiostose): relato de casos em dois irmãos. Radiol Bras. 2004;37:147-9.
6. Kudligi C, Bhagwat PV, Thirunavukkarasu A, Tophakhane RS. Incomplete pachydermoperiostosis Indian J Dermatol Venereol Leprol. 2010;76:307.
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