Extramammary Paget's disease of perianal región
DOI:
https://doi.org/10.29176/2590843X.1492Keywords:
Paget disease, Extramammary, Anal gland neoplasms, Adenocarcinoma, Perianal glandsAbstract
Paget's disease constitutes an intraepidermal adenocarcinoma that affects the nipple and more rarely, other extra-mammary apocrine areas. The perianal location represents 20% of extramammary cases and 1% of perianal neoplasms. In general, it is more common in postmenopausal women.
We present the clinical case of a young patient that develops a persistent plaque in the perianal region. A biopsy is taken, without suspecting the entity, and through histopathology and immunohistochemistry the diagnosis of Paget’s extramammary disease is confirmed. Compromise in other organs is ruled out and a successful surgical treatment is carried out.
Author Biographies
Nathalia Córdoba Ramírez
Médica, residente de tercer año de Dermatología. Universidad de Caldas, Manizales.
María Pineda Muñoz
Estudiante de Medicina, Universidad de Caldas, Manizales.
Andrés Felipe Toro Palacio
Estudiante de Medicina, Universidad de Caldas, Manizales.
Julia Mesa Villegas
Médica dermatóloga; dermatopatóloga; docente. Universidad de Caldas, Manizales.
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