Eccrine porocarcinoma of the face, an aggressive and unusual cutaneous tumor
DOI:
https://doi.org/10.29176/2590843X.1877Keywords:
Atypical cells, Clinical presentation, Eccrine porocarcinoma, Histopathology, Metastasis, Mohs micrographic surgery, Plaques, Polypoid lesions, Surgical treatment, Survival, Sweat gland cancer, Ulcerated nodulesAbstract
The eccrine porocarcinoma (PE) is a cancer of the sweat glands in the skin, with a diverse clinical presentation that includes plaques, ulcerated nodules, and polypoid lesions. Symptoms may involve itching, pain, and inflammation, and signs of malignancy such as ulcers, bleeding, rapid growth, or pain. Histopathology shows the proliferation of atypical cells with malignant features, including pleomorphism and nuclear hyperchromasia. It can metastasize to distant organs, with common sites being bone, bladder, retroperitoneum, and others. Survival depends on the tumor size, with worse prognosis for tumors larger than 4 cm. The primary treatment is surgical removal, especially in early stages, with lymph node dissection in cases of involvement. Mohs micrographic surgery is used for localized cases. Radiation therapy and chemotherapy may be options in metastasis or recurrence. Long-term follow-up is crucial, and ongoing research is needed to improve treatment strategies.
Author Biographies
Ana Maria Thorne Velez, Universidad del Sinú, Cartagena.
Médico general, Universidad del Sinú, Cartagena.
Hernando Thorné-Vélez, Universidad Libre de Barranquilla.
Residente, cuarto año de Cirugía General, Universidad Libre de Barranquilla.
Isaac Mendoza-Morales, Universidad Metropolitana de Barranquilla.
Estudiante, X semestre de Medicina, Universidad Metropolitana de Barranquilla.
Alejandro Bedoya-Rinaldi, Universidad Libre de Barranquilla.
Residente, tercer año de Cirugía General, Universidad Libre de Barranquilla.
Samuel Morales-Naranjo, Instituto Nacional de Cancerología.
Médico patólogo, Instituto Nacional de Cancerología.
Andrey Moreno-Torres, Instituto Nacional de Cancerología.
Cirujano de cabeza y cuello, Instituto Nacional de Cancerología.
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Sánchez-Morales GE, Álvarez-Bautista FE, Aguilar-Romaro JM, Vélez-Valle A, Montante-Montes de Oca D, Alfaro-Goldaracena A. Porocarcinoma ecrino. Tumor infrecuente de los anexos cutáneos. Gaceta Mexicana de Oncologia. 2020 May 8;19(91).
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