Paniculitis citofágica histiocítica asociada a leucemia mieloide crónica
Resumen
La paniculitis citofágica histiocítica es una rara alteración mediada inmunitariamente, que puede tener un curso indolente o ser fatal cuando se acompaña de síndrome hemofagocítico.
Presentamos el caso de una mujer con paniculitis citofágica histiocítica asociada a leucemia mieloide aguda.
Referencias bibliográficas
2. Kouris E, Giansante E. Síndrome de activación macrofágica. Med Cutan Iber Lat Am. 2006;34:145-54.
3. Requena L, Sánchez Yus E. Panniculitis. Mostly lobular panniculitis. J Am Acad Dermatol. 2001;45:325-61.
4. Perniciaro C, Winkelmann RK, Ehrhardt DR. Fatal systemic cytophagic histiocytic panniculitis: a histopathologic and immunohistochemical study of multiple organ sites. J Am Acad Dermatol. 1994;31:901-5.
5. Harada H, Iwatsuki K, Kaneko F. Detection of Epstein-Barr virus genes in malignant lymphoma with clinical and histologic features of cytophagic histiocytic panniculitis. J Am Acad Dermatol. 1994;31:379-83.
6. Iwatsuki K, Harada H, Ohtsuka M, Han G, Kaneko F. Latent Epstein-Barr virus infection is frequently detected in subcutaneous lymphoma associated with hemophagocytosis but not in nonfatal cytophagic histiocytic panniculitis. Arch Dermatol. 1997;133:787-8.
7. Craig AJ, Cualing H, Thomas G, Lamerson C, Smith R. Cytophagic histiocytic panniculitis –a syndrome associated with benign and malignant panniculitis: Case comparison and review of the literature. J Am Acad Dermatol. 1998;39:721-36.
8. Marzano AV, Berti E, Paulli M, Caputo R. Cytophagic histiocytic panniculitis and subcutaneous panniculitis-like T-cell lymphoma: report of 7 cases. Arch Dermatol. 2000;136:889-96.
9. Barron DR, Davis BR, Pomeranz JR, Hines JD, Park CH. Cytophagic histiocytic panniculitis. A variant of malignant histiocytosis. Cancer. 1985;55:2538-42.
10. Ito M, Ohira H, Miyata M, Suzuki T, Sato Y, Kaise S, et al. Cytophagic histiocytic panniculitis improved by combined CHOP and cyclosporin A treatment. Intern Med. 1999;38:296-301.